Chargement en cours...

A novel biochemically salvageable animal model of hyperammonemia devoid of N-acetylglutamate synthase

All knockout mouse models of urea cycle disorders die in the neonatal period or shortly thereafter. Since N-acetylglutamate synthase (NAGS) deficiency in humans can be effectively treated with N-carbamyl-L-glutamate (NCG), we sought to develop a mouse model of this disorder that could be rescued by...

Description complète

Enregistré dans:
Détails bibliographiques
Auteurs principaux: Senkevitch, Emilee, Cabrera-Luque, Juan, Morizono, Hiroki, Caldovic, Ljubica, Tuchman, Mendel
Format: Artigo
Langue:Inglês
Publié: 2012
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC3356441/
https://ncbi.nlm.nih.gov/pubmed/22503289
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ymgme.2012.03.004
Tags: Ajouter un tag
Pas de tags, Soyez le premier à ajouter un tag!