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Distinct gene-specific mechanisms of arrhythmia revealed by cardiac gene transfer of two long QT disease genes, HERG and KCNE1

The long QT syndrome (LQTS) is a heritable disorder that predisposes to sudden cardiac death. LQTS is caused by mutations in ion channel genes including HERG and KCNE1, but the precise mechanisms remain unclear. To clarify this situation we injected adenoviral vectors expressing wild-type or LQT mut...

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Autors principals: Hoppe, Uta C., Marbán, Eduardo, Johns, David C.
Format: Artigo
Idioma:Inglês
Publicat: The National Academy of Sciences 2001
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC33210/
https://ncbi.nlm.nih.gov/pubmed/11320260
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.091239098
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