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Hematopoietic defects in rps29 mutant zebrafish depend upon p53 activation

Disruption of ribosomal proteins is associated with hematopoietic phenotypes in cell culture and animal models. Mutations in ribosomal proteins are seen in patients with Diamond Blackfan anemia (DBA), a rare congenital disease characterized by red cell aplasia and distinctive craniofacial anomalies....

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Autori principali: Taylor, Alison M., Humphries, Jessica M., White, Richard M., Murphey, Ryan D., Burns, Caroline E., Zon, Leonard I.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2011
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3310385/
https://ncbi.nlm.nih.gov/pubmed/22120640
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.exphem.2011.11.007
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