Cargando...

Glutaredoxin 2 prevents aggregation of mutant SOD1 in mitochondria and abolishes its toxicity

Vulnerability of motoneurons in amyotrophic lateral sclerosis (ALS) arises from a combination of several mechanisms, including protein misfolding and aggregation, mitochondrial dysfunction and oxidative damage. Protein aggregates are found in motoneurons in models for ALS linked to a mutation in the...

Descrición completa

Gardado en:
Detalles Bibliográficos
Main Authors: Ferri, Alberto, Fiorenzo, Paolo, Nencini, Monica, Cozzolino, Mauro, Pesaresi, Maria Grazia, Valle, Cristiana, Sepe, Sara, Moreno, Sandra, Carrì, Maria Teresa
Formato: Artigo
Idioma:Inglês
Publicado: Oxford University Press 2010
Assuntos:
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC3298854/
https://ncbi.nlm.nih.gov/pubmed/20829229
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddq383
Tags: Engadir etiqueta
Sen Etiquetas, Sexa o primeiro en etiquetar este rexistro!