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Non-human primate model of amyotrophic lateral sclerosis with cytoplasmic mislocalization of TDP-43

Amyotrophic lateral sclerosis is a fatal neurodegenerative disease characterized by progressive motoneuron loss. Redistribution of transactive response deoxyribonucleic acid-binding protein 43 from the nucleus to the cytoplasm and the presence of cystatin C-positive Bunina bodies are considered path...

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Autori principali: Uchida, Azusa, Sasaguri, Hiroki, Kimura, Nobuyuki, Tajiri, Mio, Ohkubo, Takuya, Ono, Fumiko, Sakaue, Fumika, Kanai, Kazuaki, Hirai, Takashi, Sano, Tatsuhiko, Shibuya, Kazumoto, Kobayashi, Masaki, Yamamoto, Mariko, Yokota, Shigefumi, Kubodera, Takayuki, Tomori, Masaki, Sakaki, Kyohei, Enomoto, Mitsuhiro, Hirai, Yukihiko, Kumagai, Jiro, Yasutomi, Yasuhiro, Mochizuki, Hideki, Kuwabara, Satoshi, Uchihara, Toshiki, Mizusawa, Hidehiro, Yokota, Takanori
Natura: Artigo
Lingua:Inglês
Pubblicazione: Oxford University Press 2012
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3286326/
https://ncbi.nlm.nih.gov/pubmed/22252998
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/brain/awr348
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