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Physiological characterization of human muscle acetylcholine receptors from ALS patients

Amyotrophic lateral sclerosis (ALS) is characterized by progressive degeneration of motor neurons leading to muscle paralysis. Research in transgenic mice suggests that the muscle actively contributes to the disease onset, but such studies are difficult to pursue in humans and in vitro models would...

Πλήρης περιγραφή

Αποθηκεύτηκε σε:
Λεπτομέρειες βιβλιογραφικής εγγραφής
Κύριοι συγγραφείς: Palma, Eleonora, Inghilleri, Maurizio, Conti, Luca, Deflorio, Cristina, Frasca, Vittorio, Manteca, Alessia, Pichiorri, Floriana, Roseti, Cristina, Torchia, Gregorio, Limatola, Cristina, Grassi, Francesca, Miledi, Ricardo
Μορφή: Artigo
Γλώσσα:Inglês
Έκδοση: National Academy of Sciences 2011
Θέματα:
Διαθέσιμο Online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3250127/
https://ncbi.nlm.nih.gov/pubmed/22128328
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1117975108
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