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Ataxin-3 Deubiquitination Is Coupled to Parkin Ubiquitination via E2 Ubiquitin-conjugating Enzyme

We reported previously that parkin, a Parkinson disease-associated E3 ubiquitin-ligase interacts with ataxin-3, a deubiquitinating enzyme associated with Machado-Joseph disease. Ataxin-3 was found to counteract parkin self-ubiquitination both in vitro and in cells. Moreover, ataxin-3-dependent deubi...

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Autors principals: Durcan, Thomas M., Kontogiannea, Maria, Bedard, Nathalie, Wing, Simon S., Fon, Edward A.
Format: Artigo
Idioma:Inglês
Publicat: American Society for Biochemistry and Molecular Biology 2012
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3249107/
https://ncbi.nlm.nih.gov/pubmed/22081612
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.M111.288449
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