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Johanson-Blizzard syndrome

Johanson-Blizzard syndrome (JBS) is a rare autosomal recessive disease characterized by exocrine pancreatic insufficiency, hypoplastic or aplastic nasal alae, cutis aplasia on the scalp, and other features including developmental delay, failure to thrive, hearing loss, mental retardation, hypothyroi...

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Autores principales: Almashraki, Nabeel, Abdulnabee, Mukarram Zainuddin, Sukalo, Maja, Alrajoudi, Abdullah, Sharafadeen, Iman, Zenker, Martin
Formato: Artigo
Lenguaje:Inglês
Publicado: Baishideng Publishing Group Co., Limited 2011
Materias:
Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3208372/
https://ncbi.nlm.nih.gov/pubmed/22072859
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3748/wjg.v17.i37.4247
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