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Genomic imprinting at a boundary element flanking the SDHD locus

Germline mutations in SDHD, a mitochondrial complex II (succinate dehydrogenase) subunit gene at chromosome band 11q23, cause highly penetrant paraganglioma (PGL) tumors when transmitted through fathers. In contrast, maternal transmission rarely, if ever, leads to tumor development. The mechanism un...

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Autors principals: Baysal, Bora E., McKay, Sharen E., Kim, Yoon Jung, Zhang, Zimei, Alila, Linda, Willett-Brozick, Joan E., Pacak, Karel, Kim, Tae Hoon, Shadel, Gerald S.
Format: Artigo
Idioma:Inglês
Publicat: Oxford University Press 2011
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3196894/
https://ncbi.nlm.nih.gov/pubmed/21862453
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddr376
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