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Increased hedgehog signaling in postnatal kidney results in aberrant activation of nephron developmental programs

Hedgehog (Hh) is a core signaling pathway implicated in fundamental processes during embryonic kidney development. We previously found that loss-of-function mutations in the transcription factor GLIS2, a putative vertebrate ortholog of Drosophila Ci, cause nephronophthisis type 7 in humans and mice....

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Autors principals: Li, Binghua, Rauhauser, Alysha A., Dai, Julie, Sakthivel, Ramanavelan, Igarashi, Peter, Jetten, Anton M., Attanasio, Massimo
Format: Artigo
Idioma:Inglês
Publicat: Oxford University Press 2011
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3188992/
https://ncbi.nlm.nih.gov/pubmed/21816948
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddr339
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