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Mechanism of PrP‐Amyloid Formation in Mice Without Transmissible Spongiform Encephalopathy

Gerstmann–Sträussler–Scheinker (GSS) P102L disease is a familial form of a transmissible spongiform encephalopathy (TSE) that can present with or without vacuolation of neuropil. Inefficient disease transmission into 101LL transgenic mice was previously observed from GSS P102L without vacuolation. H...

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Autores principales: Jeffrey, Martin, McGovern, Gillian, Chambers, Emily V., King, Declan, González, Lorenzo, Manson, Jean C., Ghetti, Bernardino, Piccardo, Pedro, Barron, Rona M.
Formato: Artigo
Lenguaje:Inglês
Publicado: Blackwell Publishing Ltd 2011
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3182302/
https://ncbi.nlm.nih.gov/pubmed/21645162
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1111/j.1750-3639.2011.00508.x
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