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Classical and Neonatal Marfan Syndrome Mutations in Fibrillin-1 Cause Differential Protease Susceptibilities and Protein Function

Mutations in fibrillin-1 give rise to Marfan syndrome (MFS) characterized by vascular, skeletal, and ocular abnormalities. Fibrillins form the backbone of extracellular matrix microfibrils in tissues including blood vessels, bone, and skin. They are crucial for regulating elastic fiber biogenesis an...

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Bibliografische gegevens
Hoofdauteurs: Kirschner, Ryan, Hubmacher, Dirk, Iyengar, Garud, Kaur, Jasvir, Fagotto-Kaufmann, Christine, Brömme, Dieter, Bartels, Rainer, Reinhardt, Dieter P.
Formaat: Artigo
Taal:Inglês
Gepubliceerd in: American Society for Biochemistry and Molecular Biology 2011
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Online toegang:https://ncbi.nlm.nih.gov/pmc/articles/PMC3173189/
https://ncbi.nlm.nih.gov/pubmed/21784848
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.M111.221804
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