Cargando...

Lysosomal Lipid Storage Diseases

Lysosomal lipid storage diseases, or lipidoses, are inherited metabolic disorders in which typically lipids accumulate in cells and tissues. Complex lipids, such as glycosphingolipids, are constitutively degraded within the endolysosomal system by soluble hydrolytic enzymes with the help of lipid bi...

Descripción completa

Guardado en:
Detalles Bibliográficos
Autores principales: Schulze, Heike, Sandhoff, Konrad
Formato: Artigo
Lenguaje:Inglês
Publicado: Cold Spring Harbor Laboratory Press 2011
Materias:
Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3098676/
https://ncbi.nlm.nih.gov/pubmed/21502308
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1101/cshperspect.a004804
Etiquetas: Agregar Etiqueta
Sin Etiquetas, Sea el primero en etiquetar este registro!