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Inherited dysfunction of Sarcoplasmic Reticulum Ca(2+) Handling and Arrhythmogenesis

Catecholaminergic polymorphic ventricular tachycardia (CPVT) is an inherited arrhythmogenic disease occurring in patients with a structurally normal heart: the disease is characterized by life threatening arrhythmias elicited by stress and emotion. In 2001 the ryanodine receptor was identified as th...

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Autores principales: Priori, Silvia G, Chen, S. R. Wayne
Formato: Artigo
Lenguaje:Inglês
Publicado: 2011
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3085083/
https://ncbi.nlm.nih.gov/pubmed/21454795
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1161/CIRCRESAHA.110.226845
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