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Optimization of the Degenerated Interfacial ATP Binding Site Improves the Function of Disease-related Mutant Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Channels

The cystic fibrosis transmembrane conductance regulator (CFTR) chloride channel, an ATP binding cassette (ABC) protein whose defects cause the deadly genetic disease cystic fibrosis (CF), encompasses two nucleotide binding domains (NBD1 and NBD2). Recent studies indicate that in the presence of ATP,...

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Autors principals: Tsai, Ming-Feng, Jih, Kang-Yang, Shimizu, Hiroyasu, Li, Min, Hwang, Tzyh-Chang
Format: Artigo
Idioma:Inglês
Publicat: American Society for Biochemistry and Molecular Biology 2010
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2988371/
https://ncbi.nlm.nih.gov/pubmed/20861014
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.M110.172817
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