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Mutation R184Q of connexin 26 in hearing loss patients has a dominant-negative effect on connexin 26 and connexin 30

Hearing impairment is the most common sensory disorder worldwide. In a recent study, the authors have shown that a heterozygous missense mutation, p.R184Q, in the connexin 26 (Cx26) is causally related to hearing loss. However, the functional change in the Cx26R184Q mutant remains unknown. This stud...

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Autores principales: Su, Ching-Chyuan, Li, Shuan-Yow, Su, Mao-Chang, Chen, Wei-Chi, Yang, Jiann-Jou
Formato: Artigo
Lenguaje:Inglês
Publicado: Nature Publishing Group 2010
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2987407/
https://ncbi.nlm.nih.gov/pubmed/20442751
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/ejhg.2010.50
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