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Transport of dibasic amino acids, cystine, and tryptophan by cultured human fibroblasts: absence of a defect in cystinuria and Hartnup disease

Transport of lysine, arginine, cystine, and tryptophan was studied in cultured skin fibroblasts from normal controls and from patients with cystinuria and Hartnup disease. Each of these amino acids was accumulated against concentration gradients by energy-dependent, saturable mechanisms. Lysine and...

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Pubblicato in:J Clin Invest
Autori principali: Groth, Ulrich, Rosenberg, Leon E.
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society for Clinical Investigation 1972
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Accesso online:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC292370/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/5054467/
https://ncbi.nlm.nih.govhttps://doi.org/10.1172/JCI107020
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