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Age-related motor neuron degeneration in DNA repair-deficient Ercc1 mice

Degeneration of motor neurons contributes to senescence-associated loss of muscle function and underlies human neurodegenerative conditions such as amyotrophic lateral sclerosis and spinal muscular atrophy. The identification of genetic factors contributing to motor neuron vulnerability and degenera...

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Autori principali: de Waard, Monique C., van der Pluijm, Ingrid, Zuiderveen Borgesius, Nils, Comley, Laura H., Haasdijk, Elize D., Rijksen, Yvonne, Ridwan, Yanto, Zondag, Gerben, Hoeijmakers, Jan H. J., Elgersma, Ype, Gillingwater, Thomas H., Jaarsma, Dick
Natura: Artigo
Lingua:Inglês
Pubblicazione: Springer-Verlag 2010
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2923326/
https://ncbi.nlm.nih.gov/pubmed/20602234
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/s00401-010-0715-9
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