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Clinical Manifestations, Etiology, and Pathogenesis of the Hyper IgE Syndromes

Autosomal dominant Hyper IgE syndrome (AD-HIES) is a rare primary immunodeficiency characterized by eczema, recurrent skin and lung infections, elevated serum IgE, and various connective tissue, skeletal, and vascular abnormalities. Mutations in Signal transducer and activator of transcription 3 (ST...

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Dades bibliogràfiques
Autors principals: Freeman, Alexandra F., Holland, Steven M.
Format: Artigo
Idioma:Inglês
Publicat: 2009
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2919366/
https://ncbi.nlm.nih.gov/pubmed/19190525
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1203/PDR.0b013e31819dc8c5
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