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Vascular alterations upon activation of TGFβ signaling in fibroblasts - implications for systemic sclerosis

Tissue fibrosis and vascular disease are hallmarks of systemic sclerosis (SSc). Transforming growth factor β (TGFβ) is a key-player in fibroblast activation and tissue fibrosis in SSc. In contrast to fibrosis, evidence for a role of TGFβ in vascular disease of SSc is scarce. Using a transgenic mouse...

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Detalhes bibliográficos
Main Authors: Horn, Angelika, Distler, Jörg HW
Formato: Artigo
Idioma:Inglês
Publicado em: BioMed Central 2010
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC2911883/
https://ncbi.nlm.nih.gov/pubmed/20602813
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/ar3026
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