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Dystrophins, Utrophins, and Associated Scaffolding Complexes: Role in Mammalian Brain and Implications for Therapeutic Strategies

Two decades of molecular, cellular, and functional studies considerably increased our understanding of dystrophins function and unveiled the complex etiology of the cognitive deficits in Duchenne muscular dystrophy (DMD), which involves altered expression of several dystrophin-gene products in brain...

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Detalhes bibliográficos
Main Authors: Perronnet, Caroline, Vaillend, Cyrille
Formato: Artigo
Idioma:Inglês
Publicado em: Hindawi Publishing Corporation 2010
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC2896903/
https://ncbi.nlm.nih.gov/pubmed/20625423
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2010/849426
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