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Protective Protein/Cathepsin A Rescues N-glycosylation defects in Neuraminidase-1

BACKGROUND: Neuraminidase-1 (NEU1) catabolizes the hydrolysis of sialic acids from sialo-glycoconjugates. NEU1 depends on its interaction with the protective protein/cathepsin A (PPCA) for lysosomal compartmentalization and catalytic activation. Murine NEU1 contains 4 N-glycosylation sites, 3 of whi...

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Autori principali: Wang, Dongning, Zaitsev, Slava, Taylor, Garry, d’Azzo, Alessandra, Bonten, Erik
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2009
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2888680/
https://ncbi.nlm.nih.gov/pubmed/19714866
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.bbagen.2009.01.006
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