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Ubiquilin Modifies TDP-43 Toxicity in a Drosophila Model of Amyotrophic Lateral Sclerosis (ALS)

TDP-43 (43-kDa TAR DNA-binding protein) is a major constituent of ubiquitin-positive cytosolic aggregates present in neurons of patients with amyotrophic lateral sclerosis (ALS) and ubiquitin-positive fronto-temporal lobar degeneration (FTLD-U). Inherited mutations in TDP-43 have been linked to fami...

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Autors principals: Hanson, Keith A., Kim, Sang Hwa, Wassarman, David A., Tibbetts, Randal S.
Format: Artigo
Idioma:Inglês
Publicat: American Society for Biochemistry and Molecular Biology 2010
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2856981/
https://ncbi.nlm.nih.gov/pubmed/20154090
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1074/jbc.C109.078527
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