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Amelioration of Enteric Neuropathology in a Mouse Model of Niemann-Pick C by Npc1 Expression in Enteric Glia

Niemann-Pick C (NPC) disease is an autosomal recessive, lethal, neurodegenerative disorder caused by mutations in NPC1. Using the glial fibrillary acidic protein (GFAP) promoter, we demonstrated previously that astrocyte-specific expression of Npc1 decreased neuronal storage of cholesterol in Npc1(−...

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Bibliographic Details
Main Authors: Kapur, Raj, Donohue, Carolyn, Jelinek, David, Erickson, Robert P.
Format: Artigo
Language:Inglês
Published: 2009
Subjects:
Online Access:https://ncbi.nlm.nih.gov/pmc/articles/PMC2853225/
https://ncbi.nlm.nih.gov/pubmed/19472223
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1002/jnr.22126
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