Wird geladen...

Progressive renal injury from transgenic expression of human carbonic anhydrase IV folding mutants is enhanced by deficiency of p58(IPK)

Mutations in the human carbonic anhydrase IV (hCAIV) have been associated with retinal degeneration in an autosomal-dominant form of retinitis pigmentosa (RP17). Prior in vitro cell culture studies confirmed that all of the RP17-associated hCAIV mutations cause protein misfolding, leading to endopla...

Ausführliche Beschreibung

Gespeichert in:
Bibliographische Detailangaben
Hauptverfasser: Datta, Rupak, Shah, Gul N., Rubbelke, Timothy S., Waheed, Abdul, Rauchman, Michael, Goodman, Alan G., Katze, Michael G., Sly, William S.
Format: Artigo
Sprache:Inglês
Veröffentlicht: National Academy of Sciences 2010
Schlagworte:
Online Zugang:https://ncbi.nlm.nih.gov/pmc/articles/PMC2851997/
https://ncbi.nlm.nih.gov/pubmed/20308551
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1001905107
Tags: Tag hinzufügen
Keine Tags, Fügen Sie den ersten Tag hinzu!