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Joubert syndrome Arl13b functions at ciliary membranes and stabilizes protein transport in Caenorhabditis elegans

The small ciliary G protein Arl13b is required for cilium biogenesis and sonic hedgehog signaling and is mutated in patients with Joubert syndrome (JS). In this study, using Caenorhabditis elegans and mammalian cell culture systems, we investigated the poorly understood ciliary and molecular basis o...

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Autors principals: Cevik, Sebiha, Hori, Yuji, Kaplan, Oktay I., Kida, Katarzyna, Toivenon, Tiina, Foley-Fisher, Christian, Cottell, David, Katada, Toshiaki, Kontani, Kenji, Blacque, Oliver E.
Format: Artigo
Idioma:Inglês
Publicat: The Rockefeller University Press 2010
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2845074/
https://ncbi.nlm.nih.gov/pubmed/20231383
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1083/jcb.200908133
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