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Flavin Adenine Dinucleotide Rescues the Phenotype of Frataxin Deficiency

BACKGROUND: Friedreich ataxia is a neurodegenerative disease caused by the lack of frataxin, a mitochondrial protein. We previously demonstrated that frataxin interacts with complex II subunits of the electronic transport chain (ETC) and putative electronic transfer flavoproteins, suggesting that fr...

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Autori principali: Gonzalez-Cabo, Pilar, Ros, Sheila, Palau, Francesc
Natura: Artigo
Lingua:Inglês
Pubblicazione: Public Library of Science 2010
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2810331/
https://ncbi.nlm.nih.gov/pubmed/20111601
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0008872
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