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Prion-like propagation of cytosolic protein aggregates: Insights from cell culture models

Amyloid formation is a hallmark of several systemic and neurodegenerative diseases. Extracellular amyloid deposits or intracellular inclusions arise from the conformational transition of normally soluble proteins into highly ordered fibrillar aggregates. Amyloid fibrils are formed by nucleated polym...

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Autori principali: Krammer, Carmen, Schätzl, Hermann M, Vorberg, Ina
Natura: Artigo
Lingua:Inglês
Pubblicazione: Landes Bioscience 2009
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2807693/
https://ncbi.nlm.nih.gov/pubmed/19901539
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