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Nephronophthisis: Disease Mechanisms of a Ciliopathy

Nephronophthisis (NPHP), a recessive cystic kidney disease, is the most frequent genetic cause of end-stage kidney disease in children and young adults. Positional cloning of nine genes (NPHP1-9) and functional characterization of their encoded proteins (nephrocystins) has contributed to a unifying...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Egile Nagusiak: Hildebrandt, Friedhelm, Attanasio, Massimo, Otto, Edgar
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: 2008
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC2807379/
https://ncbi.nlm.nih.gov/pubmed/19118152
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1681/ASN.2008050456
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