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Characteristics of a Large Cohort of Patients with Autoimmune Pulmonary Alveolar Proteinosis in Japan

Rationale: Acquired pulmonary alveolar proteinosis (PAP) is a syndrome characterized by pulmonary surfactant accumulation occurring in association with granulocyte/macrophage colony-stimulating factor autoantibodies (autoimmune PAP) or as a consequence of another disease (secondary PAP). Because PAP...

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Main Authors: Inoue, Yoshikazu, Trapnell, Bruce C., Tazawa, Ryushi, Arai, Toru, Takada, Toshinori, Hizawa, Nobuyuki, Kasahara, Yasunori, Tatsumi, Koichiro, Hojo, Masaaki, Ichiwata, Toshio, Tanaka, Naohiko, Yamaguchi, Etsuro, Eda, Ryosuke, Oishi, Kazunori, Tsuchihashi, Yoshiko, Kaneko, Chinatsu, Nukiwa, Toshihiro, Sakatani, Mitsunori, Krischer, Jeffrey P., Nakata, Koh
Format: Artigo
Sprog:Inglês
Udgivet: American Thoracic Society 2008
Fag:
Online adgang:https://ncbi.nlm.nih.gov/pmc/articles/PMC2720118/
https://ncbi.nlm.nih.gov/pubmed/18202348
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1164/rccm.200708-1271OC
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