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Characteristics of a Large Cohort of Patients with Autoimmune Pulmonary Alveolar Proteinosis in Japan

Rationale: Acquired pulmonary alveolar proteinosis (PAP) is a syndrome characterized by pulmonary surfactant accumulation occurring in association with granulocyte/macrophage colony-stimulating factor autoantibodies (autoimmune PAP) or as a consequence of another disease (secondary PAP). Because PAP...

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Autores principales: Inoue, Yoshikazu, Trapnell, Bruce C., Tazawa, Ryushi, Arai, Toru, Takada, Toshinori, Hizawa, Nobuyuki, Kasahara, Yasunori, Tatsumi, Koichiro, Hojo, Masaaki, Ichiwata, Toshio, Tanaka, Naohiko, Yamaguchi, Etsuro, Eda, Ryosuke, Oishi, Kazunori, Tsuchihashi, Yoshiko, Kaneko, Chinatsu, Nukiwa, Toshihiro, Sakatani, Mitsunori, Krischer, Jeffrey P., Nakata, Koh
Formato: Artigo
Lenguaje:Inglês
Publicado: American Thoracic Society 2008
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2720118/
https://ncbi.nlm.nih.gov/pubmed/18202348
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1164/rccm.200708-1271OC
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