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Interferon-γ-Jak-Stat Signaling in Pulmonary Lymphangioleiomyomatosis and Renal Angiomyolipoma: A Potential Therapeutic Target

Pulmonary lymphangioleiomyomatosis (LAM) and renal angiomyolipoma (AML) are proliferative lesions that occur in sporadic patients, and at much higher frequency in patients with tuberous sclerosis (TSC). The TSC1 and TSC2 genes play a critical role in their pathogenesis. Here we report a marked decre...

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Detaylı Bibliyografya
Asıl Yazarlar: El-Hashemite, Nisreen, Kwiatkowski, David J.
Materyal Türü: Artigo
Dil:Inglês
Baskı/Yayın Bilgisi: American Thoracic Society 2005
Konular:
Online Erişim:https://ncbi.nlm.nih.gov/pmc/articles/PMC2715313/
https://ncbi.nlm.nih.gov/pubmed/15994429
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1165/rcmb.2005-0152RC
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