A carregar...
Defective Surfactant Secretion in a Mouse Model of Hermansky-Pudlak Syndrome
Hermansky-Pudlak syndrome (HPS) in humans represents a family of disorders of lysosome-related organelle biogenesis associated with severe, progressive pulmonary disease. Human case reports and a mouse model of HPS, the pale ear/pearl mouse (ep/pe), exhibit giant lamellar bodies (GLB) in type II alv...
Na minha lista:
| Main Authors: | , , , , , , |
|---|---|
| Formato: | Artigo |
| Idioma: | Inglês |
| Publicado em: |
American Thoracic Society
2005
|
| Assuntos: | |
| Acesso em linha: | https://ncbi.nlm.nih.gov/pmc/articles/PMC2715302/ https://ncbi.nlm.nih.gov/pubmed/15790974 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1165/rcmb.2004-0293OC |
| Tags: |
Adicionar Tag
Sem tags, seja o primeiro a adicionar uma tag!
|