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Investigating the Conformational Stability of Prion Strains through a Kinetic Replication Model

Prion proteins are known to misfold into a range of different aggregated forms, showing different phenotypic and pathological states. Understanding strain specificities is an important problem in the field of prion disease. Little is known about which PrP(Sc) structural properties and molecular mech...

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Autors principals: Zampieri, Mattia, Legname, Giuseppe, Altafini, Claudio
Format: Artigo
Idioma:Inglês
Publicat: Public Library of Science 2009
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2697384/
https://ncbi.nlm.nih.gov/pubmed/19578427
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pcbi.1000420
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