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Dyskeratosis congenita, stem cells and telomeres

Dyskeratosis congenita (DC) is a multi-system disorder which in its classical form is characterised by abnormalities of the skin, nails and mucous membranes. In approximately 80% of cases, it is associated with bone marrow dysfunction. A variety of other abnormalities (including bone, brain, cancer,...

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Dettagli Bibliografici
Autori principali: Kirwan, Michael, Dokal, Inderjeet
Natura: Artigo
Lingua:Inglês
Pubblicazione: Elsevier Pub. Co 2009
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2686081/
https://ncbi.nlm.nih.gov/pubmed/19419704
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.bbadis.2009.01.010
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