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The loss of the snoRNP chaperone Nopp140 from Cajal bodies of patient fibroblasts correlates with the severity of spinal muscular atrophy

Spinal muscular atrophy (SMA) is a common autosomal recessive neurodegenerative disease caused by reduced survival motor neuron (SMN) levels. The assembly machinery containing SMN is implicated in the biogenesis of the spliceosomal small nuclear ribonucleoproteins (snRNPs). SMN is present in both th...

Ausführliche Beschreibung

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Bibliographische Detailangaben
Hauptverfasser: Renvoisé, Benoît, Colasse, Sabrina, Burlet, Philippe, Viollet, Louis, Meier, U. Thomas, Lefebvre, Suzie
Format: Artigo
Sprache:Inglês
Veröffentlicht: Oxford University Press 2009
Schlagworte:
Online Zugang:https://ncbi.nlm.nih.gov/pmc/articles/PMC2655770/
https://ncbi.nlm.nih.gov/pubmed/19129172
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1093/hmg/ddp009
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