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Rpe65(−/−) and Lrat(−/−) Mice: Comparable Models of Leber Congenital Amaurosis

PURPOSE: The Rpe65(−/−) mouse, used as a model for Leber congenital amaurosis, has slow rod degeneration and rapid cone loss, presumably due to the mistrafficking of cone opsins. This animal does not generate 11-cis retinal and both the loss of cones and the rod response are restored by 11-cis retin...

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Bibliographic Details
Main Authors: Fan, Jie, Rohrer, Baerbel, Frederick, Jeanne M., Baehr, Wolfgang, Crouch, Rosalie K.
Format: Artigo
Language:Inglês
Published: 2008
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Online Access:https://ncbi.nlm.nih.gov/pmc/articles/PMC2641010/
https://ncbi.nlm.nih.gov/pubmed/18296659
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1167/iovs.08-1727
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