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The Prion Protein Knockout Mouse: A Phenotype Under Challenge

The key pathogenic event in prion disease involves misfolding and aggregation of the cellular prion protein (PrP). Beyond this fundamental observation, the mechanism by which PrP misfolding in neurons leads to injury and death remains enigmatic. Prion toxicity may come about by perverting the normal...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Egile Nagusiak: Steele, Andrew D, Lindquist, Susan, Aguzzi, Adriano
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: Landes Bioscience 2007
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC2634447/
https://ncbi.nlm.nih.gov/pubmed/19164918
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