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Wolfram Syndrome (Diabetes Insipidus, Diabetes, Optic Atrophy, and Deafness): Clinical and genetic study

OBJECTIVE—Wolfram syndrome is an autosomal recessive neurodegenerative disorder characterized by diabetes insipidus, diabetes (nonautoimmune), optic atrophy, and deafness (a set of conditions referred to as DIDMOAD). The WFS1 gene is located on the short arm of chromosome 4. Wolfram syndrome prevale...

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Detalhes bibliográficos
Main Authors: d'Annunzio, Giuseppe, Minuto, Nicola, D'Amato, Elena, de Toni, Teresa, Lombardo, Fortunato, Pasquali, Lorenzo, Lorini, Renata
Formato: Artigo
Idioma:Inglês
Publicado em: American Diabetes Association 2008
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC2518337/
https://ncbi.nlm.nih.gov/pubmed/18566338
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2337/dc08-0178
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