Residual levels of tripeptidyl-peptidase I activity dramatically ameliorate disease in late infantile neuronal ceroid lipofuscinosis

Lignende værker

• Inducible transgenic expression of tripeptidyl peptidase 1 in a mouse model of late-infantile neuronal ceroid lipofuscinosis
  af: Nemtsova, Yuliya, et al.
  Udgivet: (2018)
• Dipeptidyl-peptidase I does not functionally compensate for the loss of tripeptidyl-peptidase I in the neurodegenerative disease late-infantile neuronal ceroid lipofuscinosis
  af: Kim, Kwi-Hye, et al.
  Udgivet: (2008)
• Systemic administration of tripeptidyl peptidase I in a mouse model of late infantile neuronal ceroid lipofuscinosis: effect of glycan modification.
  af: Yu Meng, et al.
  Udgivet: (2012-01-01)
• Systemic Administration of Tripeptidyl Peptidase I in a Mouse Model of Late Infantile Neuronal Ceroid Lipofuscinosis: Effect of Glycan Modification
  af: Meng, Yu, et al.
  Udgivet: (2012)
• Crystal Structure and Autoactivation Pathway of the Precursor Form of Human Tripeptidyl-peptidase 1, the Enzyme Deficient in Late Infantile Ceroid Lipofuscinosis
  af: Guhaniyogi, Jayita, et al.
  Udgivet: (2009)