Inhibition of Proteasome Activity Promotes the Correct Localization of Disease-Causing α-Sarcoglycan Mutants in HEK-293 Cells Constitutively Expressing β-, γ-, and δ-Sarcoglycan

Sarcoglycanopathies are progressive muscle-wasting disorders caused by genetic defects of four proteins, α-, β-, γ-, and δ-sarcoglycan, which are elements of a key transmembrane complex of striated muscle. The proper assembly of the sarcoglycan complex represents a critical issue of sarcoglycanopath...

Cijeli opis

Spremljeno u:
Bibliografski detalji
Glavni autori: Gastaldello, Stefano, D'Angelo, Simona, Franzoso, Susanna, Fanin, Marina, Angelini, Corrado, Betto, Romeo, Sandonà, Dorianna
Format: Artigo
Jezik:Inglês
Izdano: American Society for Investigative Pathology 2008
Teme:
Regular Articles
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC2438295/
https://ncbi.nlm.nih.gov/pubmed/18535179
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.2353/ajpath.2008.071146
Oznake: Dodaj oznaku
Bez oznaka, Budi prvi tko označuje ovaj zapis!

Similar Items