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Proteases and Cystic Fibrosis

Cystic fibrosis is the most common, inherited fatal disease in Caucasians. The major cause of morbidity and mortality is chronic lung disease due to infection and inflammation in the airways leading to bronchiectasis and respiratory failure. The signature pathologic features of CF lung disease inclu...

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Autores principales: Voynow, Judith A., Fischer, Bernard M., Zheng, Shuo
Formato: Artigo
Lenguaje:Inglês
Publicado: 2008
Materias:
Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2431113/
https://ncbi.nlm.nih.gov/pubmed/18395488
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.biocel.2008.03.003
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