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The angiotensin system mediates renal fibrosis in glycogen storage disease type Ia nephropathy

Glycogen storage disease type Ia (GSD-Ia) patients develop renal disease of unknown etiology despite intensive dietary therapies. Interestingly, renal disease in GSD-Ia shares many clinical and pathological similarities to diabetic nephropathy, providing a model to study GSD-Ia nephropathy. In this...

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Autores principales: Yiu, Wai Han, Pan, Chi-Jiunn, Ruef, Robert A., Peng, Wen-Tao, Starost, Matthew F., Mansfield, Brian C., Chou, Janice Y.
Formato: Artigo
Lenguaje:Inglês
Publicado: 2007
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC2426750/
https://ncbi.nlm.nih.gov/pubmed/18075499
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/sj.ki.5002718
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