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The Role of the Iron Transporter ABCB7 in Refractory Anemia with Ring Sideroblasts

Refractory Anemia with Ring Sideroblasts (RARS) is an acquired myelodysplastic syndrome (MDS) characterized by an excess iron accumulation in the mitochondria of erythroblasts. The pathogenesis of RARS and the cause of this unusual pattern of iron deposition remain unknown. We considered that the in...

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Autors principals: Boultwood, Jacqueline, Pellagatti, Andrea, Nikpour, Maryam, Pushkaran, Beena, Fidler, Carrie, Cattan, Helen, Littlewood, Tim J., Malcovati, Luca, Della Porta, Matteo G., Jädersten, Martin, Killick, Sally, Giagounidis, Aristoteles, Bowen, David, Hellström-Lindberg, Eva, Cazzola, Mario, Wainscoat, James S.
Format: Artigo
Idioma:Inglês
Publicat: Public Library of Science 2008
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC2276313/
https://ncbi.nlm.nih.gov/pubmed/18398482
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0001970
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