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Laminopathic mutations interfere with the assembly, localization, and dynamics of nuclear lamins

Lamins are nuclear intermediate filament proteins and the major building blocks of the nuclear lamina. Besides providing nuclear shape and mechanical stability, lamins are required for chromatin organization, transcription regulation, DNA replication, nuclear assembly, nuclear positioning, and apopt...

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Détails bibliographiques
Auteurs principaux: Wiesel, Naama, Mattout, Anna, Melcer, Shai, Melamed-Book, Naomi, Herrmann, Harald, Medalia, Ohad, Aebi, Ueli, Gruenbaum, Yosef
Format: Artigo
Langue:Inglês
Publié: National Academy of Sciences 2008
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC2224182/
https://ncbi.nlm.nih.gov/pubmed/18162544
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.0708974105
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