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Filamin B represses chondrocyte hypertrophy in a Runx2/Smad3-dependent manner
FILAMIN B, which encodes a cytoplasmic actin binding protein, is mutated in several skeletal dysplasias. To further investigate how an actin binding protein influences skeletogenesis, we generated mice lacking intact Filamin B. As observed in spondylocarpotarsal synostosis syndrome patients, Filamin...
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| Autors principals: | , , , |
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| Format: | Artigo |
| Idioma: | Inglês |
| Publicat: |
The Rockefeller University Press
2007
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| Matèries: | |
| Accés en línia: | https://ncbi.nlm.nih.gov/pmc/articles/PMC2064428/ https://ncbi.nlm.nih.gov/pubmed/17606870 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1083/jcb.200703113 |
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