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Filamin B represses chondrocyte hypertrophy in a Runx2/Smad3-dependent manner

FILAMIN B, which encodes a cytoplasmic actin binding protein, is mutated in several skeletal dysplasias. To further investigate how an actin binding protein influences skeletogenesis, we generated mice lacking intact Filamin B. As observed in spondylocarpotarsal synostosis syndrome patients, Filamin...

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Detalhes bibliográficos
Main Authors: Zheng, Lihua, Baek, Hwa-Jin, Karsenty, Gerard, Justice, Monica J.
Formato: Artigo
Idioma:Inglês
Publicado em: The Rockefeller University Press 2007
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC2064428/
https://ncbi.nlm.nih.gov/pubmed/17606870
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1083/jcb.200703113
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