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Filamin B represses chondrocyte hypertrophy in a Runx2/Smad3-dependent manner

FILAMIN B, which encodes a cytoplasmic actin binding protein, is mutated in several skeletal dysplasias. To further investigate how an actin binding protein influences skeletogenesis, we generated mice lacking intact Filamin B. As observed in spondylocarpotarsal synostosis syndrome patients, Filamin...

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Autori principali: Zheng, Lihua, Baek, Hwa-Jin, Karsenty, Gerard, Justice, Monica J.
Natura: Artigo
Lingua:Inglês
Pubblicazione: The Rockefeller University Press 2007
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2064428/
https://ncbi.nlm.nih.gov/pubmed/17606870
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1083/jcb.200703113
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