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Disease-associated mutant α-actinin-4 reveals a mechanism for regulating its F-actin-binding affinity

α-Actinin-4 is a widely expressed protein that employs an actin-binding site with two calponin homology domains to crosslink actin filaments (F-actin) in a Ca(2+)-sensitive manner in vitro. An inherited, late-onset form of kidney failure is caused by point mutations in the α-actinin-4 actin-binding...

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Autori principali: Weins, Astrid, Schlondorff, Johannes S., Nakamura, Fumihiko, Denker, Bradley M., Hartwig, John H., Stossel, Thomas P., Pollak, Martin R.
Natura: Artigo
Lingua:Inglês
Pubblicazione: National Academy of Sciences 2007
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC2042165/
https://ncbi.nlm.nih.gov/pubmed/17901210
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.0702451104
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