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Reprogramming of keratin biosynthesis by sulforaphane restores skin integrity in epidermolysis bullosa simplex

Epidermolysis bullosa simplex (EBS) is a rare inherited condition in which the epidermis loses its integrity after mechanical trauma. EBS is typified by the dysfunction of intermediate filaments in basal keratinocytes of epidermis. Most cases of EBS are due to mutations in the keratin 5 or 14 gene (...

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Main Authors: Kerns, Michelle L., DePianto, Daryle, Dinkova-Kostova, Albena T., Talalay, Paul, Coulombe, Pierre A.
Formato: Artigo
Idioma:Inglês
Publicado: National Academy of Sciences 2007
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Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC1964870/
https://ncbi.nlm.nih.gov/pubmed/17724334
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.0706486104
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