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Endocytic Trafficking of CFTR in Health and Disease

The cystic fibrosis transmembrane conductance regulator (CFTR) is a Cl-selective anion channel expressed in epithelial tissues. Mutations in CFTR lead to the debilitating genetic disease cystic fibrosis (CF). Within each epithelial cell, CFTR interacts with a large number of transient macromolecular...

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Detalhes bibliográficos
Main Authors: Ameen, Nadia, Silvis, Mark, Bradbury, Neil A.
Formato: Artigo
Idioma:Inglês
Publicado em: 2006
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC1964799/
https://ncbi.nlm.nih.gov/pubmed/17098482
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.jcf.2006.09.002
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